Chronic granulomatous disease (CGD) presenting as quotidian fever
نویسندگان
چکیده
Clinical case The patient presented with 7 days of spiking fever not responding to oral antibiotics, arthralgias and a maculous rash. Laboratory results showed leukocytosis, thrombocytosis, CrP of 240 mg/l, ESR 100 mm. The symptoms persisted under intravenous antibiotic treatment. Focus work-up gave no evidence of an infectious origin, malignancy, IBD, vasculitis, connective tissue disease or periodic fever syndrome. Due to suspicion of incomplete SOJIA a steroid pulse was given. Disease activity responded promptly, consequently methotrexate was added.
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